ePrints

End-stage cardiac failure caused by isolated ventricular noncompaction: Cardiac transplantation in a 5-year-old boy

Lookup NU author(s): Dr Doris Rassl

Downloads

Full text for this publication is not currently held within this repository. Alternative links are provided below where available.

Abstract

Isolated ventricular non-compaction (IVNC) is a rare congenital cardiomyopathy characterized by arrest in endomyocardial morphogenesis. Presenting features in children include systolic and diastolic ventricular dysfunction, cardiac arrhythmias, and thromboembolism. End-stage cardiac failure necessitating cardiac transplantation is described in adults. We report the unique case of a 5-year-old boy with IVNC and end-stage heart failure who underwent cardiac transplantation. Diagnostic echocardiographic features, gross cardiac morphology, and histopathologic findings are illustrated. Copyright (c) 2005 by the International Society for Heart and Lung Transplantation.

Publication metadata

Author(s): Vogel M, Chaudhari M, Rassl D, Mair L, Hasan A

Publication type: Article

Publication status: Published

Journal: Journal of Heart and Lung Transplantation

Year: 2005

Volume: 24

Issue: 5

Pages: 618-620

ISSN (print): 1053-2498

ISSN (electronic): 1557-3117

Publisher: Elsevier Inc.

URL: http://dx.doi.org/10.1016/j.healun.2004.01.018

DOI: 10.1016/j.healun.2004.01.018

Altmetrics

Share